Public Article
-
verified
Future plans of Treating a Case of Acquired Pure Red Cell Aplasia Secondary to Autoimmune Causes Resistant to Combinat...
ISSN: 2583 - 2778Publisher: author   
Future plans of Treating a Case of Acquired Pure Red Cell Aplasia Secondary to Autoimmune Causes Resistant to Combinat...
Indexed in
Technology and Engineering
ARTICLE-FACTOR
1.3
Article Basics Score: 3
Article Transparency Score: 2
Article Operation Score: 2
Article Articles Score: 2
Article Accessibility Score: 2
SUBMIT PAPER ASK QUESTION
International Category Code (ICC):
ICC-1802
Publisher: Genesis Scientific Publications
International Journal Address (IAA):
IAA.ZONE/2583413912778
eISSN
:
2583 - 2778
VALID
ISSN Validator
Abstract
Pure red cell aplasia (PRCA) is an orphan disease, and as such there are no rationally developed standard treatments. Most of the cases are idiopathic with a subset being antibody mediated. An overlap exists among idiopathic cases with those of T cell large granular lymphocytic leukemia, hypogamma globulinemia as well a slow grade lymphoma. Here we report a case of acquired Pure red cell aplasia (aPRCA), who did not attain Complete remission (CR) with calcineurin inhibitor (cyclosporine A) along with prednisone 50 mg od, being associated with 2 autoimmune disorders like systemic lupus erythemzatosus (SLE) with endometriomas and has now displayed partial remission (PR) with a combination of prednisolone 50mg with anabolic steroid danazol 200mg bd for 4 months along with metoclopramide 10mg od and is being continued on same therapy for minimum of 18 months for getting a CR as did another case of SLE as well as a case of anky losing spon...